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HelpCatalog ID PIPU Pipecolic Acid, Random, Urine
Reporting Name
Pipecolic Acid, UUseful For
Differentiating between disorders of peroxisomal biogenesis (eg, Zellweger syndrome) and disorders with loss of a single peroxisomal function
Detecting abnormal elevations of pipecolic acid in urine
Necessary Information
Patient's age is required.
Specimen Required
Supplies: Urine tubes, 10 mL (T068)
Container/Tube: Plastic, 10-mL urine tube
Specimen Volume: 5 mL
Collection Instructions:
1. Collect a random urine specimen.
2. No preservative.
Specimen Minimum Volume
2 mL
Specimen Stability Information
| Specimen Type | Temperature | Time | Special Container |
|---|---|---|---|
| Urine | Frozen (preferred) | 94 days | |
| Refrigerated | 14 days |
Reference Values
≤31 days: ≤223.8 nmol/mg creatinine
32 days-5 months: ≤123.1 nmol/mg creatinine
6 months-11 months: ≤45.0 nmol/mg creatinine
≥1 year: ≤5.7 nmol/mg creatinine
Day(s) Performed
Tuesday
Reject Due To
All specimens will be evaluated at Mayo Clinic Laboratories for test suitability.Specimen Type
UrineTest Classification
This test was developed and its performance characteristics determined by Mayo Clinic in a manner consistent with CLIA requirements. It has not been cleared or approved by the US Food and Drug Administration.CPT Code Information
82542
LOINC Code Information
| Test ID | Test Order Name | Order LOINC Value |
|---|---|---|
| PIPU | Pipecolic Acid, U | 33659-4 |
| Result ID | Test Result Name | Result LOINC Value |
|---|---|---|
| 81248 | Pipecolic Acid, U | 33659-4 |
| 29952 | Interpretation | 59462-2 |
| 29954 | Reviewed By | 18771-6 |
Special Instructions
Performing Laboratory
Mayo Clinic Laboratories in Rochester
Method Name
Gas Chromatography Mass Spectrometry (GC-MS)
Testing Algorithm
For more information see Epilepsy: Unexplained Refractory and/or Familial Testing Algorithm.
Forms
If not ordering electronically, complete, print, and send a Biochemical Genetics Test Request (T798) with the specimen.